An annual visit with a cardiologist specializing in adult congenital heart defects is essential for adults with a single ventricle defect. To monitor the condition, the physician may order regular imaging or other tests, such as a portable ECG called a Holter monitor or stress testing.

People with congenital heart defects have a greater risk of developing endocarditis, a bacterial infection affecting the heart. Antibiotics may be needed before dental procedures to lower the risk of infection.

Although it may be possible to have a successful pregnancy with a single ventricle defect, pregnancy is generally not recommended. It is essential to work closely with your adult congenital cardiologist and a maternal-fetal medicine specialist before and during pregnancy.